Nonsyndromic genetic hearing loss
MONDO:0019497A disease characterized by hearing loss that is not part of a larger syndrome.
Also known as: nonsyndromic deafness, nonsyndromic hearing loss, nonsyndromic genetic hearing loss, familial deafness, isolated genetic deafness, non-syndromic genetic deafness, nonsyndromic genetic deafness
67 clinical trials for this condition and its sub-types, 4 tagged with Nonsyndromic genetic hearing loss itself.
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Sub-types of Nonsyndromic genetic hearing loss
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Prelingual non-syndromic genetic hearing loss 5 trials · 37 incl. sub-types
1 sub-type
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X-linked nonsyndromic hearing loss 0 trials · 32 incl. sub-types
6 sub-types
- X-linked mixed hearing loss with perilymphatic gusher 32 trials
- X-linked hereditary sensory and autonomic neuropathy with hearing loss 0 trials
- Hearing loss, X-linked 1 0 trials
- Hearing loss, X-linked 3 0 trials
- Hearing loss, X-linked 4 0 trials
- Hearing loss, X-linked 6 0 trials
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Hearing loss, autosomal recessive 1 trial · 17 incl. sub-types
102 sub-types
- Autosomal recessive nonsyndromic hearing loss 9 9 trials
- Autosomal recessive nonsyndromic hearing loss 39 3 trials
- Autosomal recessive nonsyndromic hearing loss 1A 2 trials
- Autosomal recessive nonsyndromic hearing loss 23 1 trial
- Autosomal recessive nonsyndromic hearing loss 5 1 trial
- Autosomal recessive nonsyndromic hearing loss 93 1 trial
- Hearing loss, autosomal recessive 118, with cochlear aplasia 1 trial
- Autosomal recessive nonsyndromic hearing loss 101 0 trials
- Autosomal recessive nonsyndromic hearing loss 102 0 trials
- Autosomal recessive nonsyndromic hearing loss 103 0 trials
- Autosomal recessive nonsyndromic hearing loss 104 0 trials
- Autosomal recessive nonsyndromic hearing loss 12 0 trials
- Autosomal recessive nonsyndromic hearing loss 124 0 trials
- Autosomal recessive nonsyndromic hearing loss 13 0 trials
- Autosomal recessive nonsyndromic hearing loss 14 0 trials
- Autosomal recessive nonsyndromic hearing loss 15 0 trials
- Autosomal recessive nonsyndromic hearing loss 16 0 trials
- Autosomal recessive nonsyndromic hearing loss 17 0 trials
- Autosomal recessive nonsyndromic hearing loss 18A 0 trials
- Autosomal recessive nonsyndromic hearing loss 18B 0 trials
- Autosomal recessive nonsyndromic hearing loss 1B 0 trials
- Autosomal recessive nonsyndromic hearing loss 2 0 trials
- Autosomal recessive nonsyndromic hearing loss 20 0 trials
- Autosomal recessive nonsyndromic hearing loss 21 0 trials
- Autosomal recessive nonsyndromic hearing loss 22 0 trials
- Autosomal recessive nonsyndromic hearing loss 24 0 trials
- Autosomal recessive nonsyndromic hearing loss 25 0 trials
- Autosomal recessive nonsyndromic hearing loss 26 0 trials
- Autosomal recessive nonsyndromic hearing loss 27 0 trials
- Autosomal recessive nonsyndromic hearing loss 28 0 trials
- Autosomal recessive nonsyndromic hearing loss 29 0 trials
- Autosomal recessive nonsyndromic hearing loss 3 0 trials
- Autosomal recessive nonsyndromic hearing loss 30 0 trials
- Autosomal recessive nonsyndromic hearing loss 31 0 trials
- Autosomal recessive nonsyndromic hearing loss 32 0 trials
- Autosomal recessive nonsyndromic hearing loss 33 0 trials
- Autosomal recessive nonsyndromic hearing loss 35 0 trials
- Autosomal recessive nonsyndromic hearing loss 36 0 trials
- Autosomal recessive nonsyndromic hearing loss 37 0 trials
- Autosomal recessive nonsyndromic hearing loss 38 0 trials
- Autosomal recessive nonsyndromic hearing loss 4 0 trials
- Autosomal recessive nonsyndromic hearing loss 40 0 trials
- Autosomal recessive nonsyndromic hearing loss 42 0 trials
- Autosomal recessive nonsyndromic hearing loss 44 0 trials
- Autosomal recessive nonsyndromic hearing loss 45 0 trials
- Autosomal recessive nonsyndromic hearing loss 46 0 trials
- Autosomal recessive nonsyndromic hearing loss 47 0 trials
- Autosomal recessive nonsyndromic hearing loss 48 0 trials
- Autosomal recessive nonsyndromic hearing loss 49 0 trials
- Autosomal recessive nonsyndromic hearing loss 51 0 trials
- Autosomal recessive nonsyndromic hearing loss 53 0 trials
- Autosomal recessive nonsyndromic hearing loss 55 0 trials
- Autosomal recessive nonsyndromic hearing loss 59 0 trials
- Autosomal recessive nonsyndromic hearing loss 6 0 trials
- Autosomal recessive nonsyndromic hearing loss 61 0 trials
- Autosomal recessive nonsyndromic hearing loss 62 0 trials
- Autosomal recessive nonsyndromic hearing loss 63 0 trials
- Autosomal recessive nonsyndromic hearing loss 65 0 trials
- Autosomal recessive nonsyndromic hearing loss 66 0 trials
- Autosomal recessive nonsyndromic hearing loss 67 0 trials
- Autosomal recessive nonsyndromic hearing loss 68 0 trials
- Autosomal recessive nonsyndromic hearing loss 7 0 trials
- Autosomal recessive nonsyndromic hearing loss 70 0 trials
- Autosomal recessive nonsyndromic hearing loss 71 0 trials
- Autosomal recessive nonsyndromic hearing loss 74 0 trials
- Autosomal recessive nonsyndromic hearing loss 76 0 trials
- Autosomal recessive nonsyndromic hearing loss 77 0 trials
- Autosomal recessive nonsyndromic hearing loss 79 0 trials
- Autosomal recessive nonsyndromic hearing loss 8 0 trials
- Autosomal recessive nonsyndromic hearing loss 83 0 trials
- Autosomal recessive nonsyndromic hearing loss 84A 0 trials
- Autosomal recessive nonsyndromic hearing loss 84B 0 trials
- Autosomal recessive nonsyndromic hearing loss 85 0 trials
- Autosomal recessive nonsyndromic hearing loss 86 0 trials
- Autosomal recessive nonsyndromic hearing loss 88 0 trials
- Autosomal recessive nonsyndromic hearing loss 89 0 trials
- Autosomal recessive nonsyndromic hearing loss 91 0 trials
- Autosomal recessive nonsyndromic hearing loss 96 0 trials
- Autosomal recessive nonsyndromic hearing loss 97 0 trials
- Autosomal recessive nonsyndromic hearing loss 98 0 trials
- Hearing loss, autosomal recessive 100 0 trials
- Hearing loss, autosomal recessive 106 0 trials
- Hearing loss, autosomal recessive 107 0 trials
- Hearing loss, autosomal recessive 108 0 trials
- Hearing loss, autosomal recessive 109 0 trials
- Hearing loss, autosomal recessive 110 0 trials
- Hearing loss, autosomal recessive 111 0 trials
- Hearing loss, autosomal recessive 112 0 trials
- Hearing loss, autosomal recessive 113 0 trials
- Hearing loss, autosomal recessive 114 0 trials
- Hearing loss, autosomal recessive 115 0 trials
- Hearing loss, autosomal recessive 116 0 trials
- Hearing loss, autosomal recessive 117 0 trials
- Hearing loss, autosomal recessive 119 0 trials
- Hearing loss, autosomal recessive 120 0 trials
- Hearing loss, autosomal recessive 121 0 trials
- Hearing loss, autosomal recessive 122 0 trials
- Hearing loss, autosomal recessive 123 0 trials
- Hearing loss, autosomal recessive 125 0 trials
- Hearing loss, autosomal recessive 57 0 trials
- Hearing loss, autosomal recessive 94 0 trials
- Hearing loss, autosomal recessive 99 0 trials
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Postlingual non-syndromic genetic hearing loss 6 trials · 10 incl. sub-types
1 sub-type
- Deafness, aminoglycoside-induced 4 trials
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Autosomal dominant nonsyndromic hearing loss 1 trial · 2 incl. sub-types
75 sub-types
- Autosomal dominant nonsyndromic hearing loss 9 1 trial
- Autosomal dominant auditory neuropathy 1 0 trials
- Autosomal dominant nonsyndromic hearing loss 1 0 trials
- Autosomal dominant nonsyndromic hearing loss 10 0 trials
- Autosomal dominant nonsyndromic hearing loss 11 0 trials
- Autosomal dominant nonsyndromic hearing loss 12 0 trials
- Autosomal dominant nonsyndromic hearing loss 13 0 trials
- Autosomal dominant nonsyndromic hearing loss 15 0 trials
- Autosomal dominant nonsyndromic hearing loss 16 0 trials
- Autosomal dominant nonsyndromic hearing loss 17 0 trials
- Autosomal dominant nonsyndromic hearing loss 18 0 trials
- Autosomal dominant nonsyndromic hearing loss 20 0 trials
- Autosomal dominant nonsyndromic hearing loss 21 0 trials
- Autosomal dominant nonsyndromic hearing loss 22 0 trials
- Autosomal dominant nonsyndromic hearing loss 23 0 trials
- Autosomal dominant nonsyndromic hearing loss 24 0 trials
- Autosomal dominant nonsyndromic hearing loss 25 0 trials
- Autosomal dominant nonsyndromic hearing loss 27 0 trials
- Autosomal dominant nonsyndromic hearing loss 28 0 trials
- Autosomal dominant nonsyndromic hearing loss 2A 0 trials
- Autosomal dominant nonsyndromic hearing loss 2B 0 trials
- Autosomal dominant nonsyndromic hearing loss 30 0 trials
- Autosomal dominant nonsyndromic hearing loss 31 0 trials
- Autosomal dominant nonsyndromic hearing loss 33 0 trials
- Autosomal dominant nonsyndromic hearing loss 36 0 trials
- Autosomal dominant nonsyndromic hearing loss 3A 0 trials
- Autosomal dominant nonsyndromic hearing loss 3B 0 trials
- Autosomal dominant nonsyndromic hearing loss 40 0 trials
- Autosomal dominant nonsyndromic hearing loss 41 0 trials
- Autosomal dominant nonsyndromic hearing loss 43 0 trials
- Autosomal dominant nonsyndromic hearing loss 44 0 trials
- Autosomal dominant nonsyndromic hearing loss 47 0 trials
- Autosomal dominant nonsyndromic hearing loss 48 0 trials
- Autosomal dominant nonsyndromic hearing loss 49 0 trials
- Autosomal dominant nonsyndromic hearing loss 4A 0 trials
- Autosomal dominant nonsyndromic hearing loss 4B 0 trials
- Autosomal dominant nonsyndromic hearing loss 5 0 trials
- Autosomal dominant nonsyndromic hearing loss 50 0 trials
- Autosomal dominant nonsyndromic hearing loss 51 0 trials
- Autosomal dominant nonsyndromic hearing loss 53 0 trials
- Autosomal dominant nonsyndromic hearing loss 54 0 trials
- Autosomal dominant nonsyndromic hearing loss 56 0 trials
- Autosomal dominant nonsyndromic hearing loss 58 0 trials
- Autosomal dominant nonsyndromic hearing loss 59 0 trials
- Autosomal dominant nonsyndromic hearing loss 6 0 trials
- Autosomal dominant nonsyndromic hearing loss 64 0 trials
- Autosomal dominant nonsyndromic hearing loss 65 0 trials
- Autosomal dominant nonsyndromic hearing loss 66 0 trials
- Autosomal dominant nonsyndromic hearing loss 67 0 trials
- Autosomal dominant nonsyndromic hearing loss 68 0 trials
- Autosomal dominant nonsyndromic hearing loss 69 0 trials
- Autosomal dominant nonsyndromic hearing loss 7 0 trials
- Autosomal dominant nonsyndromic hearing loss 70 0 trials
- Hearing loss, autosomal dominant 34, with or without inflammation 0 trials
- Hearing loss, autosomal dominant 37 0 trials
- Hearing loss, autosomal dominant 71 0 trials
- Hearing loss, autosomal dominant 72 0 trials
- Hearing loss, autosomal dominant 73 0 trials
- Hearing loss, autosomal dominant 74 0 trials
- Hearing loss, autosomal dominant 75 0 trials
- Hearing loss, autosomal dominant 76 0 trials
- Hearing loss, autosomal dominant 77 0 trials
- Hearing loss, autosomal dominant 78 0 trials
- Hearing loss, autosomal dominant 79 0 trials
- Hearing loss, autosomal dominant 80 0 trials
- Hearing loss, autosomal dominant 81 0 trials
- Hearing loss, autosomal dominant 82 0 trials
- Hearing loss, autosomal dominant 83 0 trials
- Hearing loss, autosomal dominant 84 0 trials
- Hearing loss, autosomal dominant 85 0 trials
- Hearing loss, autosomal dominant 86 0 trials
- Hearing loss, autosomal dominant 87 0 trials
- Hearing loss, autosomal dominant 88 0 trials
- Hearing loss, autosomal dominant 89 0 trials
- Hearing loss, autosomal dominant 90 0 trials
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Nonsyndromic deafness, Y-linked 0 trials
2 sub-types
- Deafness, Y-linked 2 0 trials
- Hearing loss, Y-linked 1 0 trials
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New cochlear implant aims to help those with partial hearing hear better
Disease control CompletedThis study tested a new cochlear implant (CI632) in 10 adults who have some low-frequency hearing but poor high-frequency hearing. The goal was to see if the implant improves speech understanding and overall hearing. Participants received the implant and were followed to measure …
Sponsor: Cochlear • Aim: Disease control
Last updated Aug 19, 2026 00:00 UTC
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Could a Child's own cord blood stem cells restore hearing?
Disease control CompletedThis study tests whether infusing a child's own stored umbilical cord blood stem cells is safe for children with acquired sensorineural hearing loss. The trial enrolls children with moderate to profound hearing loss and aims to see if the infusion can improve inner ear function, …
Phase 1 • Sponsor: James Baumgartner, MD • Aim: Disease control
Last updated Jul 11, 2026 00:00 UTC
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Brain implant offers sound hope for deaf children born without ears
Disease control CompletedThis study tested a special hearing device called an auditory brainstem implant in 10 children aged 2 to 5 who are profoundly deaf due to missing or damaged inner ear parts. Unlike a cochlear implant, this device is placed directly on the brainstem during surgery. The main goal w…
Phase 1 • Sponsor: Laurie Eisenberg • Aim: Disease control
Last updated Jun 26, 2026 17:22 UTC
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New brain wave test could revolutionize hearing loss diagnosis
Diagnosis CompletedThis study tested a new device called CochSyn that measures brain waves to detect hearing damage. Researchers compared results from 65 adults with and without hearing difficulties. The goal was to see if the device can accurately identify different types of hearing loss and be ea…
Sponsor: University Ghent • Aim: Diagnosis
Last updated Jun 27, 2026 09:03 UTC
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Could talking it out boost hearing aid success?
Symptom relief CompletedThis trial tests whether communication training helps first-time hearing aid users with mild to moderate hearing loss adapt better. Participants receive training either in a group or one-on-one, and researchers compare their hearing-related quality of life, communication strategi…
Sponsor: University Ghent • Aim: Symptom relief
Last updated Sep 03, 2026 00:00 UTC
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New algorithm fine-tunes cochlear implants to boost hearing in noisy places
Symptom relief CompletedThis study looked at whether a computer algorithm could improve how a cochlear implant is set for people who have one implant and a hearing aid in the other ear. Nine adults with severe hearing loss took part. The goal was to see if the new settings helped them hear better in qui…
Sponsor: Centre Hospitalier Universitaire Dijon • Aim: Symptom relief
Last updated Jun 27, 2026 09:02 UTC
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Can a simple supplement quiet tinnitus and save your hearing?
Symptom relief CompletedThis study tested a daily dietary supplement called ACEMg (Soundbites) in 64 adults with hearing loss or tinnitus. Participants took the supplement for 24 weeks and completed hearing tests and symptom surveys at home using a smartphone app. The goal was to see if the supplement c…
Sponsor: Keep Hearing, Inc. • Aim: Symptom relief
Last updated Jun 27, 2026 08:07 UTC
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Acupuncture meets modern medicine: can a herb injection ease hearing loss and vertigo?
Symptom relief CompletedThis completed study tested whether adding gastrodin acupoint injections to standard care helps people with sudden hearing loss and vertigo. One hundred adults received either standard therapy alone or standard therapy plus injections into specific acupuncture points over four we…
Sponsor: The First Hospital of Hebei Medical University • Aim: Symptom relief
Last updated Jun 27, 2026 08:04 UTC
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Can virtual reality train cochlear implant users to hear where sounds are?
Symptom relief CompletedThis study tested a new virtual reality rehab program for adults with two cochlear implants who struggle to locate where sounds come from. Twelve participants completed 8 sessions over a month, using head movements and joystick feedback to practice sound localization. The goal wa…
Sponsor: Hospices Civils de Lyon • Aim: Symptom relief
Last updated Jun 26, 2026 14:15 UTC
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Scientists hunt for genes behind hearing loss and dizziness
Knowledge-focused CompletedThis study aims to find the genetic causes of hereditary hearing loss and balance disorders. Researchers will study families with these conditions, collecting medical history, blood or cheek swabs, hearing and balance tests, and sometimes scans. The goal is to identify genes and …
Sponsor: National Institute on Deafness and Other Communication Disorders (NIDCD) • Aim: Knowledge-focused
Last updated Sep 18, 2026 00:00 UTC
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Massive gene hunt for deafness in pakistan could unlock new clues
Knowledge-focused CompletedThis study aims to find the genes that cause inherited hearing loss by analyzing DNA from 24,000 people in large Pakistani families. Researchers will compare affected and unaffected family members to identify new deafness genes. The goal is to improve genetic testing and counseli…
Sponsor: National Institute on Deafness and Other Communication Disorders (NIDCD) • Aim: Knowledge-focused
Last updated Sep 17, 2026 00:00 UTC
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Scientists hunt for genes behind inner ear malformation
Knowledge-focused CompletedThis study looked at 324 people with hearing loss and an inner ear problem called enlarged vestibular aqueducts. Researchers collected DNA, hearing tests, and scans to find genes that may cause the condition. The goal was to learn more about why it happens, not to test a treatmen…
Sponsor: National Institute on Deafness and Other Communication Disorders (NIDCD) • Aim: Knowledge-focused
Last updated Aug 06, 2026 00:00 UTC
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Electrical fingerprints may reveal hidden scarring in cochlear implant patients
Knowledge-focused CompletedThis study investigates whether a quick, painless electrical measurement called transimpedance matrix (TIM) can detect scar tissue (fibrosis) that sometimes forms inside the cochlea after cochlear implant surgery. Researchers will compare TIM results with CT scans in 180 adults w…
Sponsor: University Hospital, Montpellier • Aim: Knowledge-focused
Last updated Jul 11, 2026 00:00 UTC
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Simple signs and amplifiers may cut hospital delirium
Knowledge-focused CompletedThis study looked at whether hearing and vision loss are linked to delirium (sudden confusion) in older hospital patients. Over 1,500 participants answered screening questions and had their hearing and vision tested. In a smaller trial, researchers tested if posting communication…
Sponsor: Johns Hopkins University • Aim: Knowledge-focused
Last updated Jun 27, 2026 12:04 UTC
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Inner ear secrets: study aims to predict who will hear better with hearing aids
Knowledge-focused CompletedThis completed study enrolled 186 people with mild to moderate hearing loss to understand how damage to inner ear sensory cells and auditory neurons affects speech understanding, especially in noisy environments. Participants were fitted with hearing aids and tested on speech rec…
Sponsor: Steward St. Elizabeth's Medical Center of Boston, Inc. • Aim: Knowledge-focused
Last updated Jun 27, 2026 11:01 UTC
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Scientists hunt for gene behind severe childhood deafness
Knowledge-focused CompletedThis completed study looked at 150 children with severe to profound hearing loss to find how many have a specific genetic form called DFNB9. Researchers collected medical and genetic data from routine care. The goal was to better understand this condition and pave the way for fut…
Sponsor: Assistance Publique - Hôpitaux de Paris • Aim: Knowledge-focused
Last updated Jun 27, 2026 09:05 UTC
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Silent reading: deaf brains rewire for words
Knowledge-focused CompletedThis study looked at how deaf people who were born deaf process reading in their brains. Researchers used brain scans to compare deaf and hearing readers. The goal was to understand how the brain adapts to reading without ever hearing speech sounds. 60 adults who are deaf and hav…
Sponsor: University Hospital, Strasbourg, France • Aim: Knowledge-focused
Last updated Jun 27, 2026 08:05 UTC
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Study tracks how cochlear implants affect Kids' brain and speech over 3 years
Knowledge-focused CompletedThis study followed 50 children who received cochlear implants, measuring their brain's electrical responses to sounds and comparing them with speech and language test results over three years. The goal was to see if certain brain wave patterns could predict how well a child deve…
Sponsor: Assistance Publique - Hôpitaux de Paris • Aim: Knowledge-focused
Last updated Jun 26, 2026 15:59 UTC