Nonsyndromic genetic hearing loss
MONDO:0019497A disease characterized by hearing loss that is not part of a larger syndrome.
Also known as: nonsyndromic deafness, nonsyndromic hearing loss, nonsyndromic genetic hearing loss, familial deafness, isolated genetic deafness, non-syndromic genetic deafness, nonsyndromic genetic deafness
67 clinical trials for this condition and its sub-types, 4 tagged with Nonsyndromic genetic hearing loss itself.
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Sub-types of Nonsyndromic genetic hearing loss
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Prelingual non-syndromic genetic hearing loss 5 trials · 37 incl. sub-types
1 sub-type
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X-linked nonsyndromic hearing loss 0 trials · 32 incl. sub-types
6 sub-types
- X-linked mixed hearing loss with perilymphatic gusher 32 trials
- X-linked hereditary sensory and autonomic neuropathy with hearing loss 0 trials
- Hearing loss, X-linked 1 0 trials
- Hearing loss, X-linked 3 0 trials
- Hearing loss, X-linked 4 0 trials
- Hearing loss, X-linked 6 0 trials
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Hearing loss, autosomal recessive 1 trial · 17 incl. sub-types
102 sub-types
- Autosomal recessive nonsyndromic hearing loss 9 9 trials
- Autosomal recessive nonsyndromic hearing loss 39 3 trials
- Autosomal recessive nonsyndromic hearing loss 1A 2 trials
- Autosomal recessive nonsyndromic hearing loss 23 1 trial
- Autosomal recessive nonsyndromic hearing loss 5 1 trial
- Autosomal recessive nonsyndromic hearing loss 93 1 trial
- Hearing loss, autosomal recessive 118, with cochlear aplasia 1 trial
- Autosomal recessive nonsyndromic hearing loss 101 0 trials
- Autosomal recessive nonsyndromic hearing loss 102 0 trials
- Autosomal recessive nonsyndromic hearing loss 103 0 trials
- Autosomal recessive nonsyndromic hearing loss 104 0 trials
- Autosomal recessive nonsyndromic hearing loss 12 0 trials
- Autosomal recessive nonsyndromic hearing loss 124 0 trials
- Autosomal recessive nonsyndromic hearing loss 13 0 trials
- Autosomal recessive nonsyndromic hearing loss 14 0 trials
- Autosomal recessive nonsyndromic hearing loss 15 0 trials
- Autosomal recessive nonsyndromic hearing loss 16 0 trials
- Autosomal recessive nonsyndromic hearing loss 17 0 trials
- Autosomal recessive nonsyndromic hearing loss 18A 0 trials
- Autosomal recessive nonsyndromic hearing loss 18B 0 trials
- Autosomal recessive nonsyndromic hearing loss 1B 0 trials
- Autosomal recessive nonsyndromic hearing loss 2 0 trials
- Autosomal recessive nonsyndromic hearing loss 20 0 trials
- Autosomal recessive nonsyndromic hearing loss 21 0 trials
- Autosomal recessive nonsyndromic hearing loss 22 0 trials
- Autosomal recessive nonsyndromic hearing loss 24 0 trials
- Autosomal recessive nonsyndromic hearing loss 25 0 trials
- Autosomal recessive nonsyndromic hearing loss 26 0 trials
- Autosomal recessive nonsyndromic hearing loss 27 0 trials
- Autosomal recessive nonsyndromic hearing loss 28 0 trials
- Autosomal recessive nonsyndromic hearing loss 29 0 trials
- Autosomal recessive nonsyndromic hearing loss 3 0 trials
- Autosomal recessive nonsyndromic hearing loss 30 0 trials
- Autosomal recessive nonsyndromic hearing loss 31 0 trials
- Autosomal recessive nonsyndromic hearing loss 32 0 trials
- Autosomal recessive nonsyndromic hearing loss 33 0 trials
- Autosomal recessive nonsyndromic hearing loss 35 0 trials
- Autosomal recessive nonsyndromic hearing loss 36 0 trials
- Autosomal recessive nonsyndromic hearing loss 37 0 trials
- Autosomal recessive nonsyndromic hearing loss 38 0 trials
- Autosomal recessive nonsyndromic hearing loss 4 0 trials
- Autosomal recessive nonsyndromic hearing loss 40 0 trials
- Autosomal recessive nonsyndromic hearing loss 42 0 trials
- Autosomal recessive nonsyndromic hearing loss 44 0 trials
- Autosomal recessive nonsyndromic hearing loss 45 0 trials
- Autosomal recessive nonsyndromic hearing loss 46 0 trials
- Autosomal recessive nonsyndromic hearing loss 47 0 trials
- Autosomal recessive nonsyndromic hearing loss 48 0 trials
- Autosomal recessive nonsyndromic hearing loss 49 0 trials
- Autosomal recessive nonsyndromic hearing loss 51 0 trials
- Autosomal recessive nonsyndromic hearing loss 53 0 trials
- Autosomal recessive nonsyndromic hearing loss 55 0 trials
- Autosomal recessive nonsyndromic hearing loss 59 0 trials
- Autosomal recessive nonsyndromic hearing loss 6 0 trials
- Autosomal recessive nonsyndromic hearing loss 61 0 trials
- Autosomal recessive nonsyndromic hearing loss 62 0 trials
- Autosomal recessive nonsyndromic hearing loss 63 0 trials
- Autosomal recessive nonsyndromic hearing loss 65 0 trials
- Autosomal recessive nonsyndromic hearing loss 66 0 trials
- Autosomal recessive nonsyndromic hearing loss 67 0 trials
- Autosomal recessive nonsyndromic hearing loss 68 0 trials
- Autosomal recessive nonsyndromic hearing loss 7 0 trials
- Autosomal recessive nonsyndromic hearing loss 70 0 trials
- Autosomal recessive nonsyndromic hearing loss 71 0 trials
- Autosomal recessive nonsyndromic hearing loss 74 0 trials
- Autosomal recessive nonsyndromic hearing loss 76 0 trials
- Autosomal recessive nonsyndromic hearing loss 77 0 trials
- Autosomal recessive nonsyndromic hearing loss 79 0 trials
- Autosomal recessive nonsyndromic hearing loss 8 0 trials
- Autosomal recessive nonsyndromic hearing loss 83 0 trials
- Autosomal recessive nonsyndromic hearing loss 84A 0 trials
- Autosomal recessive nonsyndromic hearing loss 84B 0 trials
- Autosomal recessive nonsyndromic hearing loss 85 0 trials
- Autosomal recessive nonsyndromic hearing loss 86 0 trials
- Autosomal recessive nonsyndromic hearing loss 88 0 trials
- Autosomal recessive nonsyndromic hearing loss 89 0 trials
- Autosomal recessive nonsyndromic hearing loss 91 0 trials
- Autosomal recessive nonsyndromic hearing loss 96 0 trials
- Autosomal recessive nonsyndromic hearing loss 97 0 trials
- Autosomal recessive nonsyndromic hearing loss 98 0 trials
- Hearing loss, autosomal recessive 100 0 trials
- Hearing loss, autosomal recessive 106 0 trials
- Hearing loss, autosomal recessive 107 0 trials
- Hearing loss, autosomal recessive 108 0 trials
- Hearing loss, autosomal recessive 109 0 trials
- Hearing loss, autosomal recessive 110 0 trials
- Hearing loss, autosomal recessive 111 0 trials
- Hearing loss, autosomal recessive 112 0 trials
- Hearing loss, autosomal recessive 113 0 trials
- Hearing loss, autosomal recessive 114 0 trials
- Hearing loss, autosomal recessive 115 0 trials
- Hearing loss, autosomal recessive 116 0 trials
- Hearing loss, autosomal recessive 117 0 trials
- Hearing loss, autosomal recessive 119 0 trials
- Hearing loss, autosomal recessive 120 0 trials
- Hearing loss, autosomal recessive 121 0 trials
- Hearing loss, autosomal recessive 122 0 trials
- Hearing loss, autosomal recessive 123 0 trials
- Hearing loss, autosomal recessive 125 0 trials
- Hearing loss, autosomal recessive 57 0 trials
- Hearing loss, autosomal recessive 94 0 trials
- Hearing loss, autosomal recessive 99 0 trials
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Postlingual non-syndromic genetic hearing loss 6 trials · 10 incl. sub-types
1 sub-type
- Deafness, aminoglycoside-induced 4 trials
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Autosomal dominant nonsyndromic hearing loss 1 trial · 2 incl. sub-types
75 sub-types
- Autosomal dominant nonsyndromic hearing loss 9 1 trial
- Autosomal dominant auditory neuropathy 1 0 trials
- Autosomal dominant nonsyndromic hearing loss 1 0 trials
- Autosomal dominant nonsyndromic hearing loss 10 0 trials
- Autosomal dominant nonsyndromic hearing loss 11 0 trials
- Autosomal dominant nonsyndromic hearing loss 12 0 trials
- Autosomal dominant nonsyndromic hearing loss 13 0 trials
- Autosomal dominant nonsyndromic hearing loss 15 0 trials
- Autosomal dominant nonsyndromic hearing loss 16 0 trials
- Autosomal dominant nonsyndromic hearing loss 17 0 trials
- Autosomal dominant nonsyndromic hearing loss 18 0 trials
- Autosomal dominant nonsyndromic hearing loss 20 0 trials
- Autosomal dominant nonsyndromic hearing loss 21 0 trials
- Autosomal dominant nonsyndromic hearing loss 22 0 trials
- Autosomal dominant nonsyndromic hearing loss 23 0 trials
- Autosomal dominant nonsyndromic hearing loss 24 0 trials
- Autosomal dominant nonsyndromic hearing loss 25 0 trials
- Autosomal dominant nonsyndromic hearing loss 27 0 trials
- Autosomal dominant nonsyndromic hearing loss 28 0 trials
- Autosomal dominant nonsyndromic hearing loss 2A 0 trials
- Autosomal dominant nonsyndromic hearing loss 2B 0 trials
- Autosomal dominant nonsyndromic hearing loss 30 0 trials
- Autosomal dominant nonsyndromic hearing loss 31 0 trials
- Autosomal dominant nonsyndromic hearing loss 33 0 trials
- Autosomal dominant nonsyndromic hearing loss 36 0 trials
- Autosomal dominant nonsyndromic hearing loss 3A 0 trials
- Autosomal dominant nonsyndromic hearing loss 3B 0 trials
- Autosomal dominant nonsyndromic hearing loss 40 0 trials
- Autosomal dominant nonsyndromic hearing loss 41 0 trials
- Autosomal dominant nonsyndromic hearing loss 43 0 trials
- Autosomal dominant nonsyndromic hearing loss 44 0 trials
- Autosomal dominant nonsyndromic hearing loss 47 0 trials
- Autosomal dominant nonsyndromic hearing loss 48 0 trials
- Autosomal dominant nonsyndromic hearing loss 49 0 trials
- Autosomal dominant nonsyndromic hearing loss 4A 0 trials
- Autosomal dominant nonsyndromic hearing loss 4B 0 trials
- Autosomal dominant nonsyndromic hearing loss 5 0 trials
- Autosomal dominant nonsyndromic hearing loss 50 0 trials
- Autosomal dominant nonsyndromic hearing loss 51 0 trials
- Autosomal dominant nonsyndromic hearing loss 53 0 trials
- Autosomal dominant nonsyndromic hearing loss 54 0 trials
- Autosomal dominant nonsyndromic hearing loss 56 0 trials
- Autosomal dominant nonsyndromic hearing loss 58 0 trials
- Autosomal dominant nonsyndromic hearing loss 59 0 trials
- Autosomal dominant nonsyndromic hearing loss 6 0 trials
- Autosomal dominant nonsyndromic hearing loss 64 0 trials
- Autosomal dominant nonsyndromic hearing loss 65 0 trials
- Autosomal dominant nonsyndromic hearing loss 66 0 trials
- Autosomal dominant nonsyndromic hearing loss 67 0 trials
- Autosomal dominant nonsyndromic hearing loss 68 0 trials
- Autosomal dominant nonsyndromic hearing loss 69 0 trials
- Autosomal dominant nonsyndromic hearing loss 7 0 trials
- Autosomal dominant nonsyndromic hearing loss 70 0 trials
- Hearing loss, autosomal dominant 34, with or without inflammation 0 trials
- Hearing loss, autosomal dominant 37 0 trials
- Hearing loss, autosomal dominant 71 0 trials
- Hearing loss, autosomal dominant 72 0 trials
- Hearing loss, autosomal dominant 73 0 trials
- Hearing loss, autosomal dominant 74 0 trials
- Hearing loss, autosomal dominant 75 0 trials
- Hearing loss, autosomal dominant 76 0 trials
- Hearing loss, autosomal dominant 77 0 trials
- Hearing loss, autosomal dominant 78 0 trials
- Hearing loss, autosomal dominant 79 0 trials
- Hearing loss, autosomal dominant 80 0 trials
- Hearing loss, autosomal dominant 81 0 trials
- Hearing loss, autosomal dominant 82 0 trials
- Hearing loss, autosomal dominant 83 0 trials
- Hearing loss, autosomal dominant 84 0 trials
- Hearing loss, autosomal dominant 85 0 trials
- Hearing loss, autosomal dominant 86 0 trials
- Hearing loss, autosomal dominant 87 0 trials
- Hearing loss, autosomal dominant 88 0 trials
- Hearing loss, autosomal dominant 89 0 trials
- Hearing loss, autosomal dominant 90 0 trials
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Nonsyndromic deafness, Y-linked 0 trials
2 sub-types
- Deafness, Y-linked 2 0 trials
- Hearing loss, Y-linked 1 0 trials
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Can a spinal injection restore movement after paralysis?
Cure Not yet recruitingThis phase 3 trial tests whether an experimental drug called KP-100IT, injected into the spinal fluid, can help people with severe acute spinal cord injuries regain function. Participants, aged 18 to 89 with a complete loss of motor and sensory function (AIS grade A), receive fiv…
Phase 3 • Sponsor: Kringle Pharma, Inc. • Aim: Cure
Last updated Jul 25, 2026 00:00 UTC
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New cell therapy aims to boost hearing restoration in cochlear implant patients
Disease control Not yet recruitingThis early-stage trial tests a new cell therapy called Rincell-1 for adults with certain types of hearing loss who are getting a cochlear implant. The study will compare the safety and early effectiveness of receiving the cell therapy plus the implant versus the implant alone. Ab…
Phase 1/2 • Sponsor: Rinri Therapeutics • Aim: Disease control
Last updated Aug 13, 2026 00:00 UTC
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Could an app tune your hearing aids as well as an audiologist?
Disease control Not yet recruitingThis trial tests whether two self-assessment methods in a smartphone app can generate hearing aid settings that match those from a standard hearing test. Adults with perceived mild-to-moderate hearing loss will use the app to self-test their hearing and also undergo conventional …
Sponsor: Rehear Audiology Company LTD • Aim: Disease control
Last updated Aug 05, 2026 00:00 UTC
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Seeing sound: new eye on ear bones could sharpen hearing loss diagnosis
Diagnosis Not yet recruitingThis pilot study tests a new imaging system that uses OCT and vibrometry to let doctors see the middle ear bones and measure how they move in response to sound. The study enrolls 500 adults with conductive or sensorineural hearing loss. The goal is to compare these detailed motio…
Sponsor: Audioptics Medical Incorporated • Aim: Diagnosis
Last updated Jul 31, 2026 00:00 UTC
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Robot vs. surgeon: which cochlear implant method gives better hearing?
Symptom relief Not yet recruitingThis study compares two ways to insert a cochlear implant: using a robotic device or the standard manual method. Researchers want to see which approach leads to better hearing one year after surgery. The study will enroll 32 adults with hearing loss, randomly assigning them to on…
Sponsor: AdventHealth • Aim: Symptom relief
Last updated Jun 27, 2026 08:08 UTC
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Could remote Check-Ups replace frequent clinic visits for cochlear implant users?
Symptom relief Not yet recruitingThis study tests a new care pathway for adults getting a cochlear implant. Instead of the usual nine clinic visits in the first year, the new plan uses early activation of the implant and remote monitoring visits. The goal is to see if this approach is at least as good for hearin…
Sponsor: Hospices Civils de Lyon • Aim: Symptom relief
Last updated Jun 26, 2026 15:51 UTC
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Real-World data sheds light on Long-Term cochlear implant performance
Knowledge-focused Not yet recruitingThis study looks back at the medical records of 200 people who received a SONATA 2 cochlear implant. The goal is to understand how well the implant works over time in real-world settings, including speech recognition in quiet and noisy environments. Researchers will also analyze …
Sponsor: MED-EL Elektromedizinische Geräte GesmbH • Aim: Knowledge-focused
Last updated Aug 12, 2026 00:00 UTC
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Which ear gets the implant? new study aims to reduce dizziness
Knowledge-focused Not yet recruitingThis study looks at 10 adults over 50 with hearing loss and one weak balance ear. It compares implanting the device in the weak-balance ear versus the good-balance ear. The goal is to see if choosing the weaker side helps reduce dizziness after surgery.
Sponsor: University of Virginia • Aim: Knowledge-focused
Last updated Jun 27, 2026 11:00 UTC