Primary cutaneous amyloidosis

MONDO:0015301

Cutaneous amyloidosis refers to a variety of skin diseases characterized histologically by the extracellular accumulation of amyloid deposits in the dermis. Rare forms include lichen amyloidosus, X-linked reticulate pigmentary disorder, primary localized cutaneous nodular amyloidosis, and macular amyloidosis.

Also known as: primary localised cutaneous amyloidosis, primary localized cutaneous amyloidosis, PLCA, familial primary localised cutaneous amyloidosis, familial primary localized cutaneous amyloidosis, amyloidosis IX, amyloidosis familial cutaneous lichen, amyloidosis, primary localised cutaneous

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