Primary adrenal insufficiency
MONDO:0015128A hormonal disorder that occurs when the adrenal glands fail to release adequate amounts of glucocorticoids (cortisol), mineralocorticoids (aldosterone, 11-deoxycorticosterone), and androgens (dehydroepiandrosterone) to meet physiologic needs, despite release of ACTH from the pituitary.
Also known as: Addison's disease
50 clinical trials for this condition and its sub-types, 5 tagged with Primary adrenal insufficiency itself.
Follow this condition to get notified about new trialsWhere it sits in the disease tree
Browse by category →Sub-types of Primary adrenal insufficiency
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Chronic primary adrenal insufficiency 6 trials · 47 incl. sub-types
8 sub-types
- Congenital adrenal hyperplasia 36 trials · 38 incl. sub-types Sub-types →
- Triple-A syndrome 3 trials
- X-linked adrenal hypoplasia congenita 0 trials Sub-types →
- Adrenocortical hypofunction, chronic primary congenital 0 trials
- Autoimmune primary adrenal insufficiency 0 trials
- Familial adrenal hypoplasia with absent pituitary luteinizing hormone 0 trials
- Familial glucocorticoid deficiency 0 trials Sub-types →
- Inherited isolated adrenal insufficiency due to partial CYP11A1 deficiency 0 trials
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Acute adrenal insufficiency 0 trials
2 sub-types
- Waterhouse-Friderichsen syndrome 0 trials
- Bilateral massive adrenal hemorrhage 0 trials
Most studied deeper sub-types
Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
(20)
Classic congenital adrenal hyperplasia
(5)
Congenital adrenal hyperplasia due to 11-beta-hydroxylase deficiency
(1)
Congenital adrenal hyperplasia due to 17-alpha-hydroxylase deficiency
(1)
Congenital adrenal hyperplasia due to 3-beta-hydroxysteroid dehydrogenase deficiency
(1)
Congenital adrenal hyperplasia due to cytochrome P450 oxidoreductase deficiency
(1)
Congenital lipoid adrenal hyperplasia due to STAR deficency
(1)
Adrenal hypoplasia, cytomegalic type
(0)
Adrenocortical unresponsiveness to ACTH with postreceptor defect
(0)
Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency, salt wasting form
(0)
Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency, simple virilizing form
(0)
Classic congenital lipoid adrenal hyperplasia due to STAR deficency
(0)
Glucocorticoid deficiency 1
(0)
Glucocorticoid deficiency 2
(0)
Glucocorticoid deficiency 3
(0)
Glucocorticoid deficiency 4
(0)
Glucocorticoid deficiency 5
(0)
Non-classic congenital adrenal hyperplasia
(0)
Non-classic congenital lipoid adrenal hyperplasia due to STAR deficency
(0)