Rare skin disease patients develop even rarer lymphoma – scientists investigate why

NCT ID NCT07477769

First seen Jun 27, 2026 · Last updated Jun 27, 2026

Summary

This study looks at the blood immune cells of 10 adults with a rare inherited skin condition called NIPAL4 ichthyosis. Researchers want to understand why three patients with this skin disease also developed a very rare lymphoma (Sezary syndrome). By describing the normal immune cell types in these patients, they hope to find clues about a possible connection. No treatment is given; only a one-time extra blood sample is taken during routine care.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

What this could lead to
If this study finds a distinct immune cell pattern, it could point toward a way to screen for lymphoma risk in people with NIPAL4 ichthyosis.
What could go wrong
This is a very small, early observational study with only 10 participants. It is not testing a treatment, so it may not lead to any direct medical changes.

This is an AI summary of the original study and may miss details. Read our disclaimer.

Get updates

Get notified about this study

Sign up to get updates when this study changes or when new studies for AUTOSOMAL RECESSIVE CONGENITAL ICHTHYOSIS WITH NIPAL4 MUTATION are added.

Our safety recommendation!

By submitting, you agree to our Terms of use

Conditions

The condition(s) this trial relates to.

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

More trials for these conditions

Other studies related to the condition(s) this trial covers.