Targeted drug cobimetinib tested for rare immune cell cancers

NCT ID NCT04079179

First seen Jun 26, 2026 · Last updated Jun 26, 2026

Summary

This phase 2 study tests the drug cobimetinib in children and adults with Langerhans cell histiocytosis and related disorders that have come back or not responded to standard treatment. Cobimetinib blocks a growth signal that goes haywire in these diseases. The study will enroll 90 participants across four groups and measure how well the drug controls the disease over one year.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance
Cobimetinib (a targeted cancer drug that blocks a protein called MEK)
What this could lead to
If it works, this could offer a new treatment option for people with hard-to-treat histiocytic disorders, potentially controlling the disease and slowing neurodegeneration.
What could go wrong
This is a mid-stage trial with only 90 participants, so results may not apply to everyone. The drug may cause side effects and may not work for all types of histiocytosis.

This is an AI summary of the original study and may miss details. Read our disclaimer.

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Conditions

The condition(s) this trial relates to.

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Arkansas Children's Hospital

    RECRUITING

    Little Rock, Arkansas, 72202, United States

  • Children's Hospital of Orange County

    RECRUITING

    Orange, California, 92868, United States

  • Children's Medical Center- UTSW

    RECRUITING

    Dallas, Texas, 75235, United States

  • Children's National Hospital

    RECRUITING

    Washington D.C., District of Columbia, 20010, United States

  • Dana Farber Cancer Institute, Boston Children's

    RECRUITING

    Boston, Massachusetts, 02215, United States

  • John Hopkins University School of Medicine

    RECRUITING

    Baltimore, Maryland, 21287, United States

  • Memorial Sloan Kettering Cancer Center

    RECRUITING

    New York, New York, 10065, United States

  • NACHO Consortium

    NOT_YET_RECRUITING

    Memphis, Tennessee, 38105, United States

  • Phoenix Children's Hospital

    RECRUITING

    Phoenix, Arizona, 85016, United States

  • Texas Children's Hospital

    RECRUITING

    Houston, Texas, 77030, United States

  • UCSF Benioff Children's Hospital

    RECRUITING

    San Francisco, California, 94158, United States

  • University of Wisconsin-American Family Children's Hospital

    TERMINATED

    Madison, Wisconsin, 53792, United States

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