Postlingual non-syndromic genetic hearing loss
MONDO:0016298Postlingual non-syndromic genetic deafness is a rare, genetically highly heterogeneous otorhinolaryngologic disease, resulting from inner and/or middle ear or hearing nerve anomalies, typically characterized by progressive, bilateral, moderate to profound hearing loss (mean sensorineural hearing impairment equal to 40 dB or more for 500-, 1,000-, and 2,000-Hz frequency tones in the better ear) which occurs after the onset of speech development and is not associated with visible external ear abnormalities or any other medical problems. Language development is not initially significantly delayed.
Also known as: isolated postlingual genetic deafness, postlingual non-syndromic genetic deafness
10 clinical trials for this condition and its sub-types.
Follow this condition — get notified about new trialsSub-types
Broader categories
-
Balance-Restoring implant trial offers hope for chronic dizziness sufferers
Disease control OngoingThis study is testing a new device called a multichannel vestibular implant for people who have lost most or all of their balance function due to inner ear damage. The implant electrically stimulates the balance nerve to help improve stability and vision during movement. Up to 30…
Phase: NA • Sponsor: Johns Hopkins University • Aim: Disease control
Last updated Jun 27, 2026 11:00 UTC
-
Brain training may boost hearing and thinking in older cochlear implant users
Symptom relief ENROLLING_BY_INVITATIONThis study tests whether an 8-week auditory-cognitive training program can improve speech recognition and cognitive function in older adults (60+) who have had a cochlear implant for 3 months to 3 years. Participants will do computer-based listening and thinking exercises at home…
Phase: NA • Sponsor: Gallaudet University • Aim: Symptom relief
Last updated Jun 27, 2026 12:02 UTC
-
Cochlear implant study tracks hearing and balance over two years
Knowledge-focused OngoingThis study follows 39 adults with severe hearing loss who are getting a cochlear implant. Researchers will test their hearing and balance at several points over two years, using both objective tests and patient questionnaires. The goal is to better understand how the implant affe…
Sponsor: Aalborg University Hospital • Aim: Knowledge-focused
Last updated Jun 27, 2026 07:53 UTC