Insulin-resistance syndrome type A

MONDO:0012520

Type A insulin-resistance syndrome belongs to the group of extreme insulin-resistance syndromes (which includes leprechaunism, the lipodystrophies, Rabson-Mendenhall syndrome and type B insulin resistance syndrome) and is characterized by the triad of hyperinsulinemia, acanthosis nigricans (skin lesions associated with insulin resistance), and signs of hyperandrogenism in females without lipodystrophy and who are not overweight.

Also known as: insulin resistant diabetes mellitus with acanthosis nigricans and hyperandrogenism, type A insulin resistance syndrome, Iran, type a, diabetes mellitus, insulin-resistant, with acanthosis nigricans, diabetes mellitus, insulin-resistant, with acanthosis nigricans, type a, insulin receptor, defect in, with insulin-resistant diabetes mellitus and acanthosis nigricans, insulin-resistant acanthosis nigricans, type A

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