New drug cocktail targets childhood cancers with missing proteins

NCT ID NCT05407441

First seen Jun 27, 2026 · Last updated Jun 27, 2026

Summary

This study tests a combination of three drugs—tazemetostat, nivolumab, and ipilimumab—in children with rare tumors that lack the INI1 or SMARCA4 proteins. The goal is to find a safe dose and see if the drugs can shrink tumors. About 49 children with specific tumor types are being enrolled.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

tazemetostat, nivolumab, and ipilimumab

What this could lead to

If this works, it could offer a new treatment option for children with rare, hard-to-treat tumors that lack certain proteins.

What could go wrong

This is an early-phase trial with only 49 participants, so results may not apply broadly. The drug combination can cause serious side effects, and it's not yet known if it will shrink tumors effectively.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

atypical teratoid rhabdoid tumor chordoma epithelioid sarcoma rhabdoid tumor rhabdoid tumor of the kidney sarcoma SMARCA4-deficient sarcoma of thorax

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Boston Children's Hospital

    Boston, Massachusetts, 02115, United States

  • Dana-Farber Cancer Institute

    Boston, Massachusetts, 02215, United States

  • Texas Children's Hospital

    Houston, Texas, 77030, United States