Gene therapy for rare brain disease tracked over years

NCT ID NCT04273243

First seen Jun 27, 2026 · Last updated Jun 27, 2026

Summary

This study follows 10 people with CLN6 Batten disease who received a single dose of gene therapy (AT-GTX-501) in an earlier trial. Researchers are checking long-term safety and how the disease progresses over time. No new treatment is given in this follow-up.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

AT-GTX-501 (gene therapy)

What this could lead to

If successful, this follow-up could show that a single dose of gene therapy safely slows or stabilizes CLN6 Batten disease over years, pointing toward a long-term treatment option.

What could go wrong

This is a very small, early-stage follow-up study with only 10 participants, so results may not apply to everyone. The gene therapy was given years ago, and long-term safety or effectiveness is still uncertain.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

ceroid lipofuscinosis, neuronal, 6A juvenile neuronal ceroid lipofuscinosis neuronal ceroid lipofuscinosis 3 neuronal ceroid lipofuscinosis, CLN6-related, domestic cat Neuronal Ceroid-Lipofuscinoses

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Nationwide Children's Hosptial

    Columbus, Ohio, 43205, United States