TNF receptor 1-associated periodic fever syndrome

MONDO:0007727

A periodic fever syndrome, characterized by recurrent fever, arthralgia, myalgia and tender skin lesions lasting for 1 to 3 weeks, associated with skin, joint, ocular and serosal inflammation and complicated by secondary amyloidosis.

Also known as: autosomal dominant familial periodic fever, FHF, Hibernian fever, familial, TNF receptor 1-associated periodic fever syndrome, TNF receptor 1-associated periodic syndrome, TNF receptor-associated periodic syndrome, TRAPS, TRAPS syndrome

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