Junctional epidermolysis bullosa, non-Herlitz type

MONDO:0009180

Junctional epidermolysis bullosa, non-Herlitz (JEB-nH) is a subtype of junctional epidermolysis bullosa (JEB) characterized by the presence of skin and mucosal blistering, nail dystrophy or nail absence and enamel hypoplasia.

Also known as: JEN-nH, JEB-I, JEB-nH, epidermolysis bullosa Junctionalis, Disentis type, epidermolysis bullosa Junctionalis, non-Herlitz type, epidermolysis bullosa Junctionalis, progressive, epidermolysis bullosa Junctionalis, severe Nonlethal, epidermolysis bullosa, generalised atrophic benign

10 clinical trials for this condition and its sub-types.

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