Glucocorticoid-remediable aldosteronism

MONDO:0007080

Familial hyperaldosteronism type I (FH-I) is a rare heritable, glucocorticoid remediable form of primary aldosteronism (PA) characterized by early-onset hypertension, hyperaldosteronism, variable hypokalemia, low plasma renin activity (PRA), and abnormal production of 18-oxocortisol and 18-hydroxycortisol.

Also known as: FH-I, FH1, GRA, aldosteronism, glucocorticoid-remediable, dexamethasone-sensitive hypertension, familial hyperaldosteronism type 1, glucocorticoid-remediable aldosteronism, glucocorticoid-sensitive hypertension

8 clinical trials for this condition and its sub-types.

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