Buschke-Ollendorff syndrome

MONDO:0008157

Buschke-Ollendorff syndrome (BOS) is a benign disorder characterized by the association of osteopoikilosis lesions (``spotted bones'') in the skeleton and connective tissue nevi in the skin.

Also known as: Buschke-Ollendorff syndrome, osteopoikilosis with or without melorheostosis, Bos, Buschke Ollendorff syndrome, Dermatoosteopoikilosis, dermatofibrosis lenticularis disseminata with osteopoikilosis, dermatofibrosis lenticularis disseminata, isolated, dermatofibrosis, disseminated with osteopoikilosis

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