Breathing device tested to slow lung decline in ALS

Copied word for word from the study's registry entry, so the wording is the study team's rather than ours.

Inclusion Criteria: * Adult patient (over 18 years old) with a diagnosis of ALS, * \- Patient who presents with an impairment of the strength of the inspiratory muscles corresponding to the degradation of the Measurement of the maximum inspiratory pressure (MIP) and/or of the inspiratory pressure during the maximum sniffle (SNIP): * Decrease in SNIP or MIP by 10% of previous values (measured at the last follow-up visit to the center in its standard care) * If it is his first consultation (no previous value) we will include patients if they have SNIP or MIP values \<90% of the theoretical values provided by the spirometer measuring the pressures. The SNIPs and MIPs (+/-1 standard deviation) must be disturbed for inclusion of the patient. * Patient not yet using RLX for lung recruitment or Patient using RLX only as a decluttering aid. * Person affiliated or beneficiary of a social security scheme. * Free, informed and written consent signed by the participant and the investigator (at the latest on the day of inclusion and before any examination required by the research). Exclusion Criteria: * Patient with advanced restrictive impairment = FVC\<50% of theoretical values on inclusion * Patient with proven alveolar hypoventilation or treated with non-invasive ventilation * Patient already treated with RLX for pulmonary recruitment * Persons referred to in Articles L1121-5 to L1121-8 of the CSP (corresponding to all protected persons: pregnant woman, parturient, breastfeeding mother, person deprived of liberty by judicial or administrative decision, minor, and person making object of a legal protection measure: guardianship or curatorship) * Patient with a contraindication to the use of RLX (1): * Pneumothorax * Known intracranial hypertension * Hemodynamic instability * Facial or skull surgery \<6 months * Tracheoesophageal fistula * Active bleeding * Untreated active tuberculosis * Rebellious Hiccup * the history of known emphysematous or bullous pathologies