Dentin dysplasia type I

MONDO:0007436

Dentin dysplasia type I (DD-I) is a rare form of dentin dysplasia (DD) characterized by sharp conical short roots or rootless teeth.

Also known as: DD-I, DTDP1, dentin dysplasia type I, dentin dysplasia, type i, with microdontia and misshapen teeth, radicular dentin dysplasia, dentin dysplasia, Shields type 1, dentin dysplasia, type 1, dentin dysplasia, type I

2 clinical trials for this condition and its sub-types, 0 tagged with Dentin dysplasia type I itself.

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Where it sits in the disease tree

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Part of

↑ Hereditary disease (18187) ↑ Dentin dysplasia (1)

Sub-types of Dentin dysplasia type I

Atypical dentin dysplasia due to SMOC2 deficiency 0 trials
Dentin dysplasia, type IB 0 trials

Including sub-types (2) Tagged with Dentin dysplasia type I (0)

Not yet recruiting 1 Completed 1

Hunting for hidden genes behind tooth defects

Knowledge-focused Completed

This study aims to discover new genes and mutations that cause isolated forms of amelogenesis imperfecta and dentinogenesis imperfecta—inherited conditions that affect tooth enamel and dentin. Researchers are using whole exome sequencing on participants who have these tooth disor…

Sponsor: Assistance Publique - Hôpitaux de Paris • Aim: Knowledge-focused

Last updated Jul 22, 2026 00:00 UTC

Dentin dysplasia type I

Where it sits in the disease tree

Hunting for hidden genes behind tooth defects