Can a shot stop ALS before it starts? new trial tests tofersen in gene carriers

NCT ID NCT04856982

First seen Jun 27, 2026 · Last updated Jun 27, 2026

Summary

This phase 3 trial tests whether the drug tofersen can delay or prevent ALS in adults who carry a SOD1 gene mutation but have no symptoms yet. About 158 participants will receive either tofersen or a placebo, and researchers will track how many develop ALS within two years. The goal is to see if early treatment can stop the disease before it takes hold.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

Tofersen (also called BIIB067 or QALSODY)

What this could lead to

If successful, this could show that starting tofersen before symptoms appear delays or prevents the onset of ALS in people with SOD1 mutations.

What could go wrong

This is an early-stage prevention study in a small, specific genetic group. It may not work for all SOD1 mutations, and long-term safety is still being studied.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

amyotrophic lateral sclerosis type 1 familial amyotrophic lateral sclerosis amyotrophic lateral sclerosis prevention target

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Austin Neuromuscular Center

    Austin, Texas, 78756, United States

  • Azienda Ospedaliero-Universitaria Città della Salute e della Scienza di Torino

    Torino, 10124, Italy

  • California Pacific Medical Center Research Institute

    San Francisco, California, 94107, United States

  • Centrum Medyczne NeuroProtect

    Warsaw, 01-684, Poland

  • Columbia University Medical center

    New York, New York, 10032, United States

  • Genge Partners

    Montreal, Quebec, H4A 3T2, Canada

  • Groupe Hospitalier Pitie-Salpetriere

    Paris, Paris, 75651, France

  • Hanyang University Seoul Hospital

    Seoul, 04763, South Korea

  • Holy Cross Hospital

    Fort Lauderdale, Florida, 33308, United States

  • HonorHealth Neurology

    Scottsdale, Arizona, 85258, United States

  • Hospital Sao Paulo

    São Paulo, São Paulo, 04037-002, Brazil

  • Hospital Universitari i Politecnic La Fe

    Valencia, 46026, Spain

  • Johns Hopkins Hospital

    Baltimore, Maryland, 21287, United States

  • Kagoshima University Hospital

    Kagoshima, Kagoshima-ken, 890-8520, Japan

  • Macquarie University Hospital

    Macquarie Park, New South Wales, 2109, Australia

  • Massachusetts General Hospital, MA

    Charlestown, Massachusetts, 02129, United States

  • Medizinische Hochschule Hannover

    Hanover, Lower Saxony, 30625, Germany

  • NeuroProtect Sp. z o.o.

    Warsaw, Masovian Voivodeship, 01-684, Poland

  • Norrlands Universitetssjukhus

    Umeå, 90185, Sweden

  • Northwestern Medicine

    Chicago, Illinois, 60611, United States

  • PSEG Centro de Pesquisa Clinica

    São Paulo, 04038-002, Brazil

  • Sunnybrook Health Sciences Centre

    Toronto, Ontario, M4N 3M5, Canada

  • The Emory Clinic

    Atlanta, Georgia, 30322-4200, United States

  • UZ Leuven

    Leuven, 3000, Belgium

  • Universitaetsklinikum Ulm

    Ulm, Baden-Wurttemberg, 89081, Germany

  • University Hospital of Umea

    Umeå, Västerbotten County, 90185, Sweden

  • University of Calgary

    Calgary, Alberta, T2N4Z6, Canada

  • University of California San Diego Medical Center

    La Jolla, California, 92093-0949, United States

  • University of Miami School of Medicine

    Miami, Florida, 33136, United States

  • University of Sheffield

    Sheffield, South Yorkshire, S10 2RX, United Kingdom

  • University of Tokyo Hospital

    Bunkyō City, Tokyo-To, 113-8655, Japan

  • Washington University School of Medicine

    St Louis, Missouri, 63110, United States