Brain gene therapy aims to silence Huntington's disease

NCT ID NCT04120493

First seen Jun 26, 2026 · Last updated Jun 27, 2026 · Updated 1 time

Summary

This early-stage trial tests a one-time gene therapy called AMT-130, injected directly into the brain, to lower the production of the harmful huntingtin protein. It involves 43 adults with early Huntington's disease. The study is primarily checking safety, but also looks for signs that the treatment might slow the disease.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

AMT-130 (a gene therapy injected into the brain to lower the harmful huntingtin protein)

What this could lead to

If successful, this could point toward a treatment that slows or stops Huntington's disease progression by reducing the toxic protein at its source.

What could go wrong

This is an early, first-in-human study with only 43 participants, so safety and effectiveness are not yet proven. Brain surgery carries risks like infection, bleeding, or swelling.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

Huntington disease

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • CenExel Rocky Mountain Clinical Research

    Englewood, Colorado, 80113, United States

  • Johns Hopkins University

    Baltimore, Maryland, 21287, United States

  • Ohio State University

    Columbus, Ohio, 43210, United States

  • Rush University Medical Center

    Chicago, Illinois, 60612, United States

  • The University of Texas

    Houston, Texas, 77030, United States

  • University of Alabama at Birmingham

    Birmingham, Alabama, 35294-0111, United States

  • University of Arizona (Surgical Site Only)

    Tucson, Arizona, 85724, United States

  • University of California, San Francisco

    San Francisco, California, 94158, United States

  • University of Michigan Department of Neurology

    Ann Arbor, Michigan, 48105, United States

  • University of Washington Medical Center

    Seattle, Washington, 98195, United States

  • Vanderbilt University Medical Center

    Nashville, Tennessee, 37232, United States

  • Virginia Commonwealth University VCU School of Medicine, Department of Neurology

    Richmond, Virginia, 23298, United States