Pulmonary venoocclusive disease 2

A rare form of pulmonary arterial hypertension (PAH) characterized by a capillary infiltration of the pulmonary interstitium, bronchioles and pleura leading to elevated pulmonary arterial resistance and right heart failure. PCH is potentially fatal.

Also known as: pulmonary capillary hemangiomatosis, PVOD2, familial pulmonary capillary hemangiomatosis, hemangiomatosis, familial pulmonary capillary, pulmonary venoocclusive disease 2, autosomal recessive

0 clinical trials for this condition and its sub-types, 0 tagged with Pulmonary venoocclusive disease 2 itself.