Kasabach-Merritt syndrome

MONDO:0007708

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma.

Also known as: Kasabach Merritt phenomenon, Kasabach Merritt syndrome, Kasabach-Merritt Phenomenon, Kasabach-Merritt syndrome, hemangioma-hemorrhage syndrome, hemangioma-thrombocytopenia syndrome, hemangiomatosis with thrombocytopenia, thrombocytopenia-hemangioma syndrome

2 clinical trials for this condition and its sub-types.

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