Isolated right ventricular hypoplasia
MONDO:0010179Isolated right ventricular hypoplasia (IRVH) is a rare congenital heart malformation characterized by underdevelopment of the right ventricle associated with patent foramen ovale or interauricular communication and normally developed tricuspid and pulmonary valves. IRVH manifests with severe cyanosis, congestive heart failure, and in severe cases, death in early infancy.
Also known as: Irvh, hypoplasia of the right ventricle, isolated hypoplasia of the right ventricle, right ventricle hypoplasia, right ventricular hypoplasia, right ventricular hypoplasia, isolated
2 clinical trials for this condition and its sub-types.
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New heart solution tested in Kids' surgery: could it offer better protection?
Disease control TerminatedThis study compares two solutions, Custodiol and Custodiol-N, used to protect the heart during surgery for children with congenital heart defects. About 100 children will receive one of the two solutions while on a heart-lung machine. The goal is to see which one is safer and bet…
Phase: PHASE2 • Sponsor: Dr. F. Köhler Chemie GmbH • Aim: Disease control
Last updated Jun 27, 2026 09:03 UTC
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Heart defect study tracks kids' outcomes 11 years after surgery
Knowledge-focused OngoingThis study looks at 237 children born with hypoplastic left heart syndrome (HLHS), a serious heart defect. Researchers compare how well the heart works at age 11 in children who received one of two different shunts during their first surgery. The goal is to understand which shunt…
Sponsor: Carelon Research • Aim: Knowledge-focused
Last updated Jun 27, 2026 07:56 UTC