Hereditary pulmonary alveolar proteinosis

Congenital pulmonary alveolar proteinosis is a very rare primary interstitial lung disease due to pulmonary surfactant accumulation within the alveolar macrophages and alveoli, characterized by a variable clinical course ranging from an asymptomatic clinical presentation and spontaneous remission, to symptoms such as dyspnea and cough, or to severe respiratory failure.

Also known as: congenital PAP, congenital pulmonary alveolar proteinosis, hereditary pulmonary alveolar proteinosis, inborn error of pulmonary surfactant metabolism, inborn error of surfactant metabolism, pulmonary alveolar proteinosis, congenital, sufactant metabolism dysfunction, pulmonary

6 clinical trials for this condition and its sub-types.