Auditory neuropathy

MONDO:0021944

A hearing disorder characterized by impaired transmission of signals through the auditory nerve, resulting in mild to severe hearing loss and poor speech perception.

Also known as: ANSD, auditory dys-synchrony, auditory neuropathy, auditory neuropathy spectrum disorder, familial auditory neuropathy, progressive auditory neuropathy

11 clinical trials for this condition and its sub-types, 7 tagged with Auditory neuropathy itself.

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Where it sits in the disease tree

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Part of

↑ Hereditary neurological disease (5791) ↑ Hearing loss disorder (442) ↑ Inherited auditory system disease (120)

Sub-types of Auditory neuropathy

Autosomal recessive nonsyndromic hearing loss 9 9 trials
X-linked hereditary sensory and autonomic neuropathy with hearing loss 0 trials
Auditory neuropathy, autosomal dominant 2 0 trials
Auditory neuropathy, autosomal dominant 3 0 trials
Autosomal dominant auditory neuropathy 1 0 trials

Including sub-types (11) Tagged with Auditory neuropathy (7)

Trials to join now! 5 Not yet recruiting 2 Not yet finished but already full! 3 Completed 1

Scientists hunt for gene behind severe childhood deafness

Knowledge-focused Completed

This completed study looked at 150 children with severe to profound hearing loss to find how many have a specific genetic form called DFNB9. Researchers collected medical and genetic data from routine care. The goal was to better understand this condition and pave the way for fut…

Sponsor: Assistance Publique - Hôpitaux de Paris • Aim: Knowledge-focused

Last updated Jun 27, 2026 09:05 UTC

Auditory neuropathy

Where it sits in the disease tree

Scientists hunt for gene behind severe childhood deafness