Peripheral primitive neuroectodermal tumor

MONDO:0018271

A small round cell tumor with neural differentiation arising from the soft tissues or bone.

Also known as: PPNET, pPNET, peripheral PNET, peripheral neuroectodermal neoplasm, peripheral neuroectodermal tumor, peripheral neuroectodermal tumour, peripheral neuroepithelioma, peripheral primitive neuroectodermal neoplasm

2739 clinical trials for this condition and its sub-types, 7 tagged with Peripheral primitive neuroectodermal tumor itself.

Follow this condition to get notified about new trials

Where it sits in the disease tree

Browse by category →

Part of

↑ Primitive neuroectodermal tumor (228) ↑ Ewing sarcoma/peripheral primitive neuroectodermal tumor (149) ↑ Peripheral nervous system cancer (66)

Sub-types of Peripheral primitive neuroectodermal tumor

Peripheral primitive neuroectodermal tumor of bone 3 trials
Peripheral primitive neuroectodermal tumor of soft tissues 3 trials
Askin tumor 0 trials

Including sub-types (2739) Tagged with Peripheral primitive neuroectodermal tumor (7)

Trials to join now! 2 Not yet finished but already full! 4 Completed 1

New drug targets tough childhood cancers with genetic flaws

Disease control Completed

This phase 2 trial tested the drug samotolisib in 18 children and young adults with advanced solid tumors, non-Hodgkin lymphoma, or histiocytic disorders that had spread, returned, or stopped responding to treatment. Only patients whose tumors had specific mutations in the TSC or…

Phase 2 • Sponsor: National Cancer Institute (NCI) • Aim: Disease control

Last updated Jun 27, 2026 12:23 UTC

Peripheral primitive neuroectodermal tumor

Where it sits in the disease tree

New drug targets tough childhood cancers with genetic flaws