Malignant perineurioma

MONDO:0016751

A very rare malignant tumor with morphologic features similar to those of benign perineurioma of soft tissue along with hypercellularity, nuclear atypia, hyperchromasia, and a high mitotic rate.

Also known as: malignant peripheral nerve sheath tumor with perineurial differentiation, malignant peripheral nerve sheath tumour with perineurial differentiation, perineurial malignant peripheral nerve sheath tumor, perineurial malignant peripheral nerve sheath tumour, perineurioma, malignant

2822 clinical trials for this condition and its sub-types, 1 tagged with Malignant perineurioma itself.

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Where it sits in the disease tree

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Part of

↑ Malignant glioma (915) ↑ Peripheral nervous system cancer (66) ↑ Perineurioma (1)

Including sub-types (2822) Tagged with Malignant perineurioma (1)

Trials to join now! 1

New hope for rare childhood cancer: drug cocktail aims to shrink tumors and prevent return

Disease control Recruiting now

This study is for children and young adults (up to age 30) with a rare type of soft tissue cancer called non-rhabdomyosarcoma. It tests whether adding the drugs pazopanib and selinexor to standard chemotherapy can improve outcomes. Participants receive treatment tailored to their…

Phase 1/2 • Sponsor: St. Jude Children's Research Hospital • Aim: Disease control

Last updated Aug 05, 2026 00:00 UTC

Malignant perineurioma

Where it sits in the disease tree

New hope for rare childhood cancer: drug cocktail aims to shrink tumors and prevent return