Epithelioid malignant peripheral nerve sheath tumor

MONDO:0004540

A rare variant of malignant peripheral nerve sheath tumor composed predominantly or exclusively of epithelioid cells.

Also known as: epithelioid MPNST, epithelioid malignant peripheral nerve sheath tumor, malignant epithelioid neoplasm of peripheral nerve sheath, malignant epithelioid neoplasm of the peripheral nerve sheath, malignant epithelioid peripheral nerve sheath neoplasm, malignant epithelioid peripheral nerve sheath tumor, malignant epithelioid peripheral nerve sheath tumour, malignant epithelioid tumor of peripheral nerve sheath

2908 clinical trials for this condition and its sub-types, 2 tagged with Epithelioid malignant peripheral nerve sheath tumor itself.

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Where it sits in the disease tree

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↑ Malignant peripheral nerve sheath tumor (38)

Including sub-types (2908) Tagged with Epithelioid malignant peripheral nerve sheath tumor (2)

Not yet finished but already full! 1 Completed 1

Experimental drug tazemetostat offered to patients with rare, aggressive tumors

Disease control Expanded access (ended)

This expanded access program provides tazemetostat, a drug that blocks a protein called EZH2, to adults with serious or life-threatening solid tumors that have lost the INI1 or SMARCA4 protein. Eligible patients must have tried other treatments without success and cannot join a f…

Sponsor: Epizyme, Inc. • Aim: Disease control

Last updated Jul 04, 2026 00:00 UTC

Epithelioid malignant peripheral nerve sheath tumor

Where it sits in the disease tree

Experimental drug tazemetostat offered to patients with rare, aggressive tumors