Bilateral striopallidodentate calcinosis

MONDO:0008947

A basal ganglia disease characterized by the accumulation of calcium deposits in different brain regions, particularly the basal ganglia and dentate nucleus, and is often associated with neurodegeneration.

Also known as: BSPDC, PFBC, Primary Familial Brain Calcification, basal ganglia calcification, basal ganglia degeneration with calcification, cerebrovascular ferrocalcinosis, primary familial brain calcification, Fahr disease

1 clinical trial for this condition and its sub-types, 1 tagged with Bilateral striopallidodentate calcinosis itself.

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↑ Hereditary neurological disease (5791) ↑ Basal ganglia disorder (1322)

Sub-types of Bilateral striopallidodentate calcinosis

Basal ganglia calcification, idiopathic, 1 0 trials
Basal ganglia calcification, idiopathic, 10, autosomal recessive 0 trials
Basal ganglia calcification, idiopathic, 11, autosomal recessive 0 trials
Basal ganglia calcification, idiopathic, 4 0 trials
Basal ganglia calcification, idiopathic, 5 0 trials
Basal ganglia calcification, idiopathic, 6 0 trials
Basal ganglia calcification, idiopathic, 7, autosomal recessive 0 trials
Basal ganglia calcification, idiopathic, 8, autosomal recessive 0 trials
Basal ganglia calcification, idiopathic, 9, autosomal recessive 0 trials
Basal ganglia calcification, idiopathic, childhood-onset 0 trials

Including sub-types (1) Tagged with Bilateral striopallidodentate calcinosis (1)

Trials to join now! 1

Could a bone drug stop brain calcium buildup in Fahr's disease?

Disease control Recruiting now

This phase 2 trial tests whether etidronate, a drug used for bone disorders, can reduce calcium deposits in the brain and slow disease progression in Fahr's disease or syndrome. 98 adults will receive either etidronate or a placebo for 12 months. The study measures changes in thi…

Phase 2 • Sponsor: UMC Utrecht • Aim: Disease control

Last updated Jun 27, 2026 09:10 UTC

Bilateral striopallidodentate calcinosis

Where it sits in the disease tree

Could a bone drug stop brain calcium buildup in Fahr's disease?