Autoimmune interstitial lung disease-arthritis syndrome
MONDO:0014629A respiratory disease characterized by interstitial lung disease (often with pulmonary hemorrhage) and inflammatory arthritis, associated with high-titer autoantibodies (including anti-nuclear and anti-neutrophil cytoplasmic antibodies, and rheumatoid factor). Patients present from infancy to adolescence with tachypnea, cough, hemoptysis, and/or joint pain. Some patients may also develop glomerular disease.
Also known as: COPA Syndrome, autoinflammation and autoimmunity, systemic, with immune dysregulation, AILJK, autoimmune interstitial lung, joint, and kidney disease
14 clinical trials for this condition and its sub-types, 3 tagged with Autoimmune interstitial lung disease-arthritis syndrome itself.
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Sub-types of Autoimmune interstitial lung disease-arthritis syndrome
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New pill aims to tame rare immune diseases
Disease control OngoingThis early-stage trial tests an experimental drug called BI 3000202 in 16 adults with rare type 1 interferonopathies, such as Aicardi-Goutières syndrome. Participants take a low dose for 4 weeks, then a higher dose for 36 weeks. The main goal is to see if the drug is safe and how…
Phase 1 • Sponsor: Boehringer Ingelheim • Aim: Disease control
Last updated Sep 17, 2026 00:00 UTC
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Breathing in xenon: a new MRI scan to see lung damage?
Knowledge-focused OngoingThis study at Duke University tests whether a special MRI scan using inhaled xenon gas can detect changes in lung function over time in people with progressive pulmonary fibrosis. Sixty adults with various types of lung scarring will have MRI scans before starting anti-fibrotic m…
Phase 2 • Sponsor: Duke University • Aim: Knowledge-focused
Last updated Jun 27, 2026 13:08 UTC