Auditory neuropathy
MONDO:0021944A hearing disorder characterized by impaired transmission of signals through the auditory nerve, resulting in mild to severe hearing loss and poor speech perception.
Also known as: ANSD, auditory dys-synchrony, auditory neuropathy, auditory neuropathy spectrum disorder, familial auditory neuropathy, progressive auditory neuropathy
11 clinical trials for this condition and its sub-types, 7 tagged with Auditory neuropathy itself.
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Sub-types of Auditory neuropathy
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Gene therapy aims to restore hearing in children born deaf
Cure Recruiting nowThis study tests a new gene therapy called DB-OTO for children with hearing loss caused by changes in the otoferlin gene. The treatment is injected into the inner ear to help restore hearing. Up to 30 children and infants will take part to check safety and how well it works.
Phase 1/2 • Sponsor: Regeneron Pharmaceuticals • Aim: Cure
Last updated Aug 07, 2026 00:00 UTC
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Gene therapy aims to restore hearing in children with rare genetic deafness
Disease control Recruiting nowThis trial tests a gene therapy called AAVAnc80-hOTOF for people with severe hearing loss caused by mutations in the otoferlin gene. The therapy is given as a single injection into the inner ear during surgery. The study will check if the treatment is safe and if it can improve h…
Phase 1/2 • Sponsor: Akouos, Inc. • Aim: Disease control
Last updated Jun 27, 2026 09:10 UTC
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Scientists track rare genetic hearing loss over time
Knowledge-focused Recruiting nowThis study follows up to 150 people with hearing loss caused by changes in the otoferlin gene. Researchers will measure hearing function using tests like auditory brainstem response (ABR) and otoacoustic emissions (OAE). The goal is to learn how this type of hearing loss changes …
Sponsor: Akouos, Inc. • Aim: Knowledge-focused
Last updated Jun 27, 2026 09:10 UTC