Can early enzyme therapy help babies with pompe disease breathe on their own?

NCT ID NCT04848779

First seen Jun 25, 2026 · Last updated Jun 27, 2026 · Updated 1 time

Summary

This study follows 16 infants aged 6 months or younger with infantile-onset Pompe disease, a rare genetic disorder that weakens muscles and breathing. All receive alglucosidase alfa (Myozyme) as part of their routine care. Researchers track how many survive without needing a breathing machine after 52 weeks of treatment, along with heart function, motor skills, and growth.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

alglucosidase alfa (enzyme replacement therapy)

What this could lead to

If successful, this could confirm that early enzyme replacement helps infants with Pompe disease survive longer without needing a breathing machine.

What could go wrong

This is a small observational study with only 16 infants, so results may not apply to all patients. The treatment requires lifelong infusions and may cause immune reactions.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

glycogen storage disease due to acid maltase deficiency, infantile onset glycogen storage disease II Glycogen Storage Disease Type II

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Advanced Medical Genetics- Site Number : 8400002

    Hawthorne, New York, 10532, United States

  • Cincinnati Children's Hospital Medical Center- Site Number : 8400001

    Cincinnati, Ohio, 45229, United States

  • Duke University Medical Center- Site Number : 8400004

    Durham, North Carolina, 27710, United States

  • Investigational Site Number : 0560001

    Leuven, 3000, Belgium

  • Investigational Site Number : 1580001

    Taipei, 100, Taiwan

  • Investigational Site Number : 2500001

    Tours, 37000, France

  • Investigational Site Number : 2760001

    Giessen, 35392, Germany

  • Investigational Site Number : 3800001

    Florence, 50139, Italy

  • Investigational Site Number : 3800002

    Monza, Monza E Brianza, 20052, Italy

  • Investigational Site Number : 5280001

    Rotterdam, 3015 CE, Netherlands

  • Investigational Site Number : 7240001

    Esplugues de Llobregat, Catalunya [Cataluña], 08950, Spain

  • Investigational Site Number : 8260001

    London, London, City of, WC1N 3JH, United Kingdom

  • Investigational Site Number : 8260002

    Manchester, M13 9WL, United Kingdom

  • Le Bonheur Children's Hospital- Site Number : 8400005

    Memphis, Tennessee, 38103, United States

  • Seattle Children's Hospital- Site Number : 8400003

    Seattle, Washington, 98105, United States