Experimental drug ataluren tested for safety in duchenne MD patients

NCT ID NCT01247207

First seen Jun 27, 2026 · Last updated Jun 27, 2026

Summary

This study tested the safety of a drug called ataluren (also known as Translarna) in 270 people with Duchenne muscular dystrophy caused by a specific type of genetic mistake (nonsense mutation). Participants had already taken ataluren in earlier studies. The goal was to monitor side effects, lab results, and physical changes over time. The drug is meant to help the body produce a working version of the dystrophin protein, which is missing in Duchenne.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

ataluren (PTC124, Translarna)

What this could lead to

If successful, this could confirm that ataluren is safe enough to use long-term for managing Duchenne muscular dystrophy in people with a specific genetic mutation.

What could go wrong

This is an open-label safety study, not designed to prove the drug works. It only includes people who already took ataluren, so results may not apply to new patients. Side effects are still possible.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

Duchenne muscular dystrophy neuromuscular disease caused by qualitative or quantitative defects of dystrophin

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Alberta Children's Hospital

    Calgary, Alberta, Canada

  • British Columbia Children's Hospital

    Vancouver, British Columbia, Canada

  • CHU de Québec - Université Laval

    Québec, Canada

  • Child Neurology Center of NW Florida NW

    Gulf Breeze, Florida, 32561, United States

  • Children's Hospital Colorado - Center for Cancer and Blood Disorders

    Aurora, Colorado, 80045, United States

  • Children's Hospital of Boston/Harvard Medical School

    Boston, Massachusetts, 02115, United States

  • Children's Hospital of East Ontario

    Ottawa, Ontario, Canada

  • Children's Hospital of Los Angeles

    Los Angeles, California, 90027, United States

  • Children's Hospital of Philadelphia

    Philadelphia, Pennsylvania, 19104, United States

  • Children's Hospital of the King's Daughters

    Norfolk, Virginia, 23507, United States

  • Childrens Medical Center Dallas

    Dallas, Texas, 75207, United States

  • Cincinnati Childrens Hospital Medical Center

    Cincinnati, Ohio, 45229, United States

  • Columbia University Pediatric Neuromuscular Center

    New York, New York, 10032, United States

  • Duke University Medical Center

    Durham, North Carolina, 27710, United States

  • London Health Sciences Centre

    London, Ontario, Canada

  • Nationwide Children's Hospital

    Columbus, Ohio, 43205, United States

  • Phoenix Childrens Hospital

    Phoenix, Arizona, 85016, United States

  • Rare Disease Research, LLC

    Atlanta, Georgia, 30329, United States

  • Rush Univ Medical Center

    Chicago, Illinois, 60612, United States

  • Seattle Children's Hospital

    Seattle, Washington, 98105, United States

  • Shriners Hospital for Children-Portland

    Portland, Oregon, 97239, United States

  • Stanford University

    Palo Alto, California, 94304, United States

  • Texas Children's Hospital

    Houston, Texas, 77030, United States

  • UCLA

    Los Angeles, California, 90095, United States

  • University of CA, San Francisco-Benioff Children's Hospital

    San Francisco, California, 94158, United States

  • University of California-Davis

    Sacramento, California, 95817, United States

  • University of Iowa Children's Hospital

    Iowa City, Iowa, 52242, United States

  • University of Kansas Medical Center

    Kansas City, Kansas, 66160, United States

  • University of Michigan

    Ann Arbor, Michigan, 48109, United States

  • University of Minnesota

    Minneapolis, Minnesota, 55455, United States

  • University of Pittsburgh Medical Center

    Pittsburgh, Pennsylvania, 16148, United States

  • University of Texas Health Science Center at San Antonio

    San Antonio, Texas, 78229, United States

  • University of Utah

    Salt Lake City, Utah, 84112, United States

  • Washington University Medical School

    St Louis, Missouri, 63110, United States