Hope for rare nerve disease: new drug targets toxic sugar buildup

NCT ID NCT05397665

First seen Jun 27, 2026 · Last updated Jun 27, 2026

Summary

This study tests an experimental drug called AT-007 (Govorestat) in 56 adults with SORD deficiency, a rare genetic condition that causes nerve damage and muscle weakness. The drug aims to lower high levels of sorbitol, a sugar that builds up and harms nerves. Researchers will measure if it improves walking speed and other daily functions over up to 24 months.

What this could mean

Our plain-language read of the trial. This is informational only — not medical advice or a prediction.

Active substance

Govorestat (AT-007), an aldose reductase inhibitor

What this could lead to

If successful, this could lead to the first approved treatment for SORD deficiency, potentially slowing or improving nerve damage and mobility.

What could go wrong

This is a mid-stage trial with only 56 participants, so results may not apply to everyone. The drug may not improve symptoms enough to be meaningful, and side effects are still being studied.

Disclaimer Read more

This is a summary of the original study . Summaries may miss details or leave out important information. Before applying or accepting participation, make sure you have read and understood the full study. Curemydisease.com takes no responsibility whatsoever for anything missed, misunderstood, or acted upon as a result of our summary — we know it does not capture everything.

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Conditions

The condition(s) this trial relates to.

neuronopathy, distal hereditary motor, autosomal recessive 8

As listed by the trial registrant

The condition terms exactly as the trial's registrant entered them.

Contacts and locations

Locations

  • Axon Clinical, s.r.o.

    Prague, Prague, 150 00, Czechia

  • Fondazione IRCCS Istituto Neurologico "Carlo Besta"

    Milan, Milano, 20133, Italy

  • Hassman Research Institute

    Berlin, New Jersey, 08009, United States

  • Massachusetts General Hospital

    Boston, Massachusetts, 02114, United States

  • University College of London

    London, London, WC1E 6BT, United Kingdom

  • University of Colorado

    Aurora, Colorado, 80045, United States

  • University of Iowa

    Iowa City, Iowa, 52242, United States

  • University of Miami

    Coral Gables, Florida, 33146, United States

  • University of Pennsylvania

    Philadelphia, Pennsylvania, 19104, United States

  • University of Rochester

    Rochester, New York, 14642, United States